{"id":4059,"date":"2026-01-27T22:02:22","date_gmt":"2026-01-27T20:02:22","guid":{"rendered":"https:\/\/life4hsp.com\/?p=4059"},"modified":"2026-01-27T22:02:22","modified_gmt":"2026-01-27T20:02:22","slug":"update-onderzoek-spg11-eerste-resultaten-veelbelovend","status":"publish","type":"post","link":"https:\/\/life4hsp.com\/es\/update-onderzoek-spg11-eerste-resultaten-veelbelovend\/","title":{"rendered":"Actualizaci\u00f3n de la investigaci\u00f3n sobre SPG11 \u2013 Primeros resultados prometedores"},"content":{"rendered":"<p data-start=\"189\" data-end=\"456\">La investigaci\u00f3n sobre un posible tratamiento para la SPG11, llevada a cabo por el <a href=\"https:\/\/parisbraininstitute.org\/\">Paris Brain Institute<\/a>, comenz\u00f3 en abril de 2025 y avanza seg\u00fan lo previsto. Se trata de investigaci\u00f3n precl\u00ednica en modelos murinos, financiada por <a href=\"https:\/\/www.eurohsp.eu\/\">Euro-HSP<\/a> y <a href=\"https:\/\/life4hsp.com\/es\/onderzoek-naar-behandeling-voor-spg11-gestart\/\">Life4HSP.<\/a><\/p>\n<p data-start=\"458\" data-end=\"809\">El estudio analiza la eficacia y la seguridad del f\u00e1rmaco venglustat. Las primeras evaluaciones en ratones muestran que el medicamento es bien tolerado y sugieren una posible mejora tanto de las funciones motoras como cognitivas. Estos resultados son cautelosamente alentadores y coinciden con hallazgos de investigaciones anteriores.<\/p>\n<p data-start=\"811\" data-end=\"1084\">En el pr\u00f3ximo per\u00edodo, el enfoque se centrar\u00e1 en continuar la investigaci\u00f3n y en recopilar datos adicionales. Estos datos son esenciales para confirmar los resultados y evaluar si es posible y responsable avanzar hacia estudios adicionales.<\/p>\n<p data-start=\"1086\" data-end=\"1282\">Seguiremos de cerca el progreso y les mantendremos informados sobre nuevos desarrollos. Gracias al apoyo de donantes y socios, esta importante investigaci\u00f3n sobre la SPG11 puede continuar.<\/p>","protected":false},"excerpt":{"rendered":"<p>Het onderzoek naar een mogelijke behandeling voor SPG11, dat wordt uitgevoerd door het Paris Brain Institute, is gestart in april 2025 en verloopt volgens planning. Dit betreft preklinisch onderzoek in muismodellen en wordt gefinancierd door Euro-HSP en Life4HSP. Binnen het onderzoek wordt gekeken naar de werking en veiligheid van het medicijn venglustat. De eerste evaluaties [&hellip;]<\/p>\n","protected":false},"author":6,"featured_media":4060,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"inline_featured_image":false,"footnotes":""},"categories":[13],"tags":[],"class_list":["post-4059","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-onderzoek"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v28.2 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Update onderzoek SPG11 \u2013 eerste resultaten veelbelovend - Life4HSP<\/title>\n<meta name=\"description\" content=\"Preklinisch onderzoek naar een mogelijke behandeling voor SPG11 laat positieve eerste signalen zien. 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