{"id":4059,"date":"2026-01-27T22:02:22","date_gmt":"2026-01-27T20:02:22","guid":{"rendered":"https:\/\/life4hsp.com\/?p=4059"},"modified":"2026-01-27T22:02:22","modified_gmt":"2026-01-27T20:02:22","slug":"update-onderzoek-spg11-eerste-resultaten-veelbelovend","status":"publish","type":"post","link":"https:\/\/life4hsp.com\/en\/update-onderzoek-spg11-eerste-resultaten-veelbelovend\/","title":{"rendered":"SPG11 Research Update \u2013 First Results Are Promising"},"content":{"rendered":"<p data-start=\"189\" data-end=\"456\">The research into a potential treatment for SPG11, conducted by <a href=\"https:\/\/parisbraininstitute.org\/\">Paris Brain Institute<\/a>, began in April 2025 and is progressing according to plan. This is preclinical research in mouse models and is funded by <a href=\"https:\/\/www.eurohsp.eu\/\">Euro-HSP<\/a> and <a href=\"https:\/\/life4hsp.com\/en\/research-to-treatment-for-spg11-started\/\">Life4HSP.<\/a><\/p>\n<p data-start=\"458\" data-end=\"809\">The study focuses on the efficacy and safety of the drug venglustat. Initial evaluations in mice show that the drug is well tolerated and suggest a possible improvement in both motor and cognitive functions. These results are cautiously encouraging and align with findings from previous studies.<\/p>\n<p data-start=\"811\" data-end=\"1084\">In the coming period, the focus will be on continuing the research and collecting additional data. These data are essential to confirm the results and to assess whether further steps toward additional studies are possible and responsible.<\/p>\n<p data-start=\"1086\" data-end=\"1282\">We will continue to closely monitor progress and keep you informed of new developments. Thanks to the support of donors and partners, this important research into SPG11 can continue.<\/p>","protected":false},"excerpt":{"rendered":"<p>Het onderzoek naar een mogelijke behandeling voor SPG11, dat wordt uitgevoerd door het Paris Brain Institute, is gestart in april 2025 en verloopt volgens planning. Dit betreft preklinisch onderzoek in muismodellen en wordt gefinancierd door Euro-HSP en Life4HSP. Binnen het onderzoek wordt gekeken naar de werking en veiligheid van het medicijn venglustat. De eerste evaluaties [&hellip;]<\/p>\n","protected":false},"author":6,"featured_media":4060,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"inline_featured_image":false,"footnotes":""},"categories":[13],"tags":[],"class_list":["post-4059","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-onderzoek"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.9 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Update onderzoek SPG11 \u2013 eerste resultaten veelbelovend - Life4HSP<\/title>\n<meta name=\"description\" content=\"Preklinisch onderzoek naar een mogelijke behandeling voor SPG11 laat positieve eerste signalen zien. 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